Familial occurrence of infantile myofibromatosis

نویسندگان
چکیده

منابع مشابه

Congenital occurrence of solitary infantile myofibromatosis of the spleen.

Infantile myofibromatosis (IM) is a rare soft tissue tumor of infancy and childhood. We report the case of a newborn girl with an abdominal tumor discovered at 32 weeks of gestation by fetal ultrasound. She underwent a laparotomy for an unexplained abdominal mass 20 days after birth. The tumor originated from the spleen and was removed by splenectomy. There were no other abnormal findings on di...

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Infantile myofibromatosis*

Infantile myofibromatosis is a mesenchymal disorder characterized by the fibrous proliferation of the skin, bone, muscle and viscera. It is the most common fibrous tumor in childhood. We present a newborn with skin and bone disease without visceral involvement, who showed good response to vinblastine and methotrexate. Clinical features, etiology, diagnosis, and treatment are reviewed.

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Infantile Myofibromatosis

Infantile myofibromatosis (IMP) is a rare tumour with a wide spectrum of disease activity ra a solitarY cutaneous nodule through to a multicentric form ,vith widespread visceral involveluent. R is charactelised by its unique ability to spontaneously regress and has a typical histological appearance of a~tin-positivefibroblasts arranged in whorls or fascicles and vessels in a pericytomatous patt...

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Infantile myofibromatosis.

Infantile myofibromatosis (IMF) is a rare tumour with a wide spectrum of disease activity ranging from a solitary cutaneous nodule through to a multicentric form with widespread visceral involvement. It is characterised by its unique ability to spontaneously regress and has a typical histological appearance of actin-positive fibroblasts arranged in whorls or fascicles and vessels in a pericytom...

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Multicentric Infantile Myofibromatosis

We present a case of multicentric infantile myofibromatosis in a 3-month-old male infant who had multiple papular lesions on his extremities and trunk and a slowly growing and bulging mass on his left occipital area since birth. His general physical condition was good and psychomotor development was normal. The diagnosis was established by histopathological and immunohistochemical studies along...

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ژورنال

عنوان ژورنال: Cancer

سال: 2010

ISSN: 0008-543X

DOI: 10.1002/cncr.2820690537